Published: 2016-12-21

Linear nevus sebaceous syndrome with lissencephaly

Poonam Sinha, Swati Kalra, Anju Aggarwal, Vinita Rathi


Linear nevus sebaceous syndrome is a congenital neurocutaneous syndrome comprising of nevus sebaceous, seizures and mental retardation. We report a 6 month old female child with a linear nevus sebaceous over the face and scalp, whose brain imaging revealed ipsilateral lissencephaly with hemimegalencephaly. Lissencephaly is rarely reported in this syndrome.


Lissencephaly, Hemimegalencephaly, Linear nevus sebaceous syndrome

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