Ectrodadactyly: a rare case report

Authors

  • Sindhu Maru Department of Pediatrics, Sree Balaji Medical College and Hospital, Chennai, Tamil Nadu
  • Thumjaa Annamalai Department of Pediatrics, Sree Balaji Medical College and Hospital, Chennai, Tamil Nadu
  • Raja Selvan R Department of Pediatrics, Sree Balaji Medical College and Hospital, Chennai, Tamil Nadu
  • Vamsi Krishna Reddy K. Department of Pediatrics, Sree Balaji Medical College and Hospital, Chennai, Tamil Nadu

DOI:

https://doi.org/10.18203/2349-3291.ijcp20162406

Keywords:

Ectrodactyly, Split hand, Foot malformation, Median Cleft

Abstract

Ectrodactyly also called as split hand or foot malformation (SHFM).Congenital absence of all or part of one or more fingers or toes is defined as Ectrodactyly. Irregular pattern of inheritance exists for ectrodactyly, may be autosomal dominant, autosomal recessive or X linked. In this condition, the median cleft of the hand gives the appearance of lobster claw-so called ‘Lobster Claw Hand’. Ectrodactyly may be very commonly associated with other anomalies of face, eyes and skeletal system. We report a rare case of unilateral ectrodactyly of right hand.

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Published

2016-12-21