DOI: http://dx.doi.org/10.18203/2349-3291.ijcp20162406

Ectrodadactyly: a rare case report

Sindhu Maru, Thumjaa Annamalai, Raja Selvan R, Vamsi Krishna Reddy K.

Abstract


Ectrodactyly also called as split hand or foot malformation (SHFM).Congenital absence of all or part of one or more fingers or toes is defined as Ectrodactyly. Irregular pattern of inheritance exists for ectrodactyly, may be autosomal dominant, autosomal recessive or X linked. In this condition, the median cleft of the hand gives the appearance of lobster claw-so called ‘Lobster Claw Hand’. Ectrodactyly may be very commonly associated with other anomalies of face, eyes and skeletal system. We report a rare case of unilateral ectrodactyly of right hand.


Keywords


Ectrodactyly, Split hand, Foot malformation, Median Cleft

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References


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