Unna Thost syndrome: a case report

Authors

  • Geetha M. Department of Paediatrics, East Point College of Medical Sciences and Research Centre, Bangalore, Karnataka, India
  • Rajeswari Bhat Department of Dermatology,East Point College of Medical Sciences and Research Centre, Bangalore, Karnataka, India
  • Kiran B. Department of Pathology, East Point College of Medical Sciences and Research Centre, Bangalore, Karnataka, India
  • Madhusmitha Jena Department of Pathology, East Point College of Medical Sciences and Research Centre, Bangalore, Karnataka, India
  • Libni D. Angel Department of Paediatrics, East Point College of Medical Sciences and Research Centre, Bangalore, Karnataka, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20192793

Keywords:

Hyperhidrosis, Epidermolysis, Palmo plantar keratoderma, Unna Thost Syndrome, Vorner

Abstract

Unna thost syndrome is Palmo Plantar Keratoderma (PPK) of diffuse non epidermolytic type inherited in autosomal dominant fashion. Authors had a seven-year-old boy born to second degree consanguineous parents had palmoplantar keratoderma with hyperhidrosis with positive family history. He was promptly diagnosed and treated with acitretin and showed improvement.

References

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Published

2019-06-27

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Case Reports