DOI: http://dx.doi.org/10.18203/2349-3291.ijcp20200130

Severe haemoptysis in a 5 year old child with Kartagener’s syndrome: case report

Mohinish S., Mallesh K., Prashanth H. K., Ravichandra K. R.

Abstract


Kartagener`s syndrome, a rare autosomal recessive disorder is a type of Primary Ciliary Dyskinesia (PCD) associated situs inversus, bronchiectasis, sinusitis and male infertility. We present a case of a 5-year-old girl who came with features of bilateral glue ear, recurrent sinusitis, recurrent hemoptysis and dextrocardia. She was diagnosed to have Kartagener`s syndrome and was evaluated for recurrent hemoptysis.


Keywords


Absent bronchus, Dextrocardia, Haemoptysis, Kartagener`s syndrome, Primary ciliary dyskinesia, Short neck

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References


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