DOI: http://dx.doi.org/10.18203/2349-3291.ijcp20200125

Acquired generalized lipodystrophy type 2-lawrence syndrome: a rare case report

Dhanalakshmi K., Mohinish S., Dakshayani B., Mallesh K.

Abstract


Lawrence syndrome (Acquired Generalized Lipodystrophy) is a rare disorder, characterized by various dermatological and systemic manifestations such as lipodystrophy, hypertriglyceridemia, hepatomegaly, acanthosis nigricans and acromegaloid features. Because of its rare occurrence we are reporting a case with similar manifestations in a 10 years old child.


Keywords


Acquired generalized lipodystrophy, Autoimmune hepatitis, Diabetes, Hyperglycemia, Lawrence syndrome, Leptins, Partial dystrophy

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