Acquired generalized lipodystrophy type 2-lawrence syndrome: a rare case report

Authors

  • Dhanalakshmi K. Department of Pediatrics, Bangalore Medical College and Research Institute, Bangalore, Karnataka, India
  • Mohinish S. Department of Pediatrics, Bangalore Medical College and Research Institute, Bangalore, Karnataka, India
  • Dakshayani B. Department of Pediatrics, Bangalore Medical College and Research Institute, Bangalore, Karnataka, India
  • Mallesh K. Department of Pediatrics, Bangalore Medical College and Research Institute, Bangalore, Karnataka, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20200125

Keywords:

Acquired generalized lipodystrophy, Autoimmune hepatitis, Diabetes, Hyperglycemia, Lawrence syndrome, Leptins, Partial dystrophy

Abstract

Lawrence syndrome (Acquired Generalized Lipodystrophy) is a rare disorder, characterized by various dermatological and systemic manifestations such as lipodystrophy, hypertriglyceridemia, hepatomegaly, acanthosis nigricans and acromegaloid features. Because of its rare occurrence we are reporting a case with similar manifestations in a 10 years old child.

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Published

2020-01-23

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Case Reports