Pituitary stalk transection syndrome

Authors

  • Gayathri Sajeevan Department of Pediatrics, Amrita Institute of Medical Sciences Kochi, Kerala
  • Sajitha Nair Department of Pediatrics, Amrita Institute of Medical Sciences Kochi, Kerala
  • Devika Geetha Department of Pediatrics, Amrita Institute of Medical Sciences Kochi, Kerala
  • Nisha Bhavani 2Department of Endocrinology, Amrita Institute of Medical Sciences Kochi, Kerala
  • C. Jayakumar Department of Pediatrics, Amrita Institute of Medical Sciences Kochi, Kerala, India
  • Suchitra Sivadas Department of Pediatrics, Amrita Institute of Medical Sciences Kochi, Kerala, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20205105

Keywords:

Growth hormone deficiency, PSTS, Short stature

Abstract

Growth hormone deficiency is one of the most common endocrinological causes for short stature. It can either be idiopathic or associated with organic causes like tumors or following surgery. One of the rare causes for growth hormone deficiency in children is pituitary stalk transection syndrome. It can be diagnosed by magnetic resonance imaging of the hypothalamus and pituitary gland which shows an ectopic or absent posterior pituitary, an absent or interrupted pituitary stalk, or small anterior pituitary in combination with growth hormone or other pituitary hormone deficiencies. Current report presents a child with pituitary stalk transection syndrome who was brought for evaluation of hypoglycemic seizures.

References

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Published

2020-11-24

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Section

Case Reports