DOI: http://dx.doi.org/10.18203/2349-3291.ijcp20211692

Ohtahara syndrome progressing to West syndrome

Tapan Patel, Shivani Patel

Abstract


West syndrome is a severe epilepsy syndrome composed of the triad of infantile spasms, hypsarrhythmia on electroencephalography (EEG) and mental retardation. It is sometimes due to the progression of a rare and fatal condition called early infantile epileptic encephalopathy (Ohtahara syndrome). Here we describe the case of a 3 year old male, who is a known case of West syndrome, presenting with recurrent breakthrough convulsions.


Keywords


Ohtahara syndrome, West syndrome, Breakthrough seizures, Rare disease

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References


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