Right pulmonary artery agenesis with transient hypothyroidism in a newborn

Authors

  • Preeti Gupta Department of of Pediatrics and Neonatology, Shri Mata Vaishno Devi Narayana Hospital, Jammu, Jammu and Kashmir, India
  • Amitabha Chattopadhyay Department of Pediatric Cardiology, Narayana Hospital, Howrah, West Bengal, India
  • Geetanjali Gupta Department of Radiology, Shri Mata Vaishno Devi Narayana Hospital, Jammu, Jammu and Kashmir, India
  • Jayita Das Department of Pediatric Cardiology, Narayana Hospital, Howrah, West Bengal, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20171737

Keywords:

Newborn, Pulmonary artery agenesis, Transient hypothyroidism

Abstract

Unilateral absence of pulmonary artery (UAPA) is a rare congenital anomaly that can present as an isolated lesion or may be associated with other Congenital heart diseases. It is usually detected in infancy or incidentally found on X ray chest in adulthood. The diagnosis of UAPA has rarely been made in a newborn. Only one case has been reported in newborn period from Belgium by F. Marchau who reported the rare occurrence of this anomaly in a 2-day old male baby. We report the rare occurrence of UAPA in a newborn female from India who presented with severe respiratory distress at birth with high cord blood TSH levels. Our case also reflects the importance of a high index of suspicion along with the value of X-ray chest and echocardiogram in the neonatal period in detection of this rare anomaly.

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Published

2017-04-25

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Section

Case Reports